Aplastic kupererwa neropa

Aplastic kupererwa neropa

Tsanangudzo yezvokurapa

Marie Curie naEleanor Roosevelt, pakati pevamwe, vakatambura nechirwere ichi chakakomba uye chisingawanzo. Aplastic - kana aplastic - anemia inoitika kana mwongo usingachagadziri zvakakwana hematopoietic stem masero. Zvisinei, aya ndiwo manyuko emasero ose eropa, ayo ari marudzi matatu: masero matsvuku eropa, masero machena eropa uye maplatelet.

Aplastic anemia saka inokonzera mapoka matatu ezviratidzo. Kutanga, izvo zvinowanzoitika kune marudzi akasiyana-siyana eanemia: kana zviratidzo zvekushayikwa kwemasero matsvuku eropa - uye naizvozvo zvekutakura kusina kukwana kweokisijeni. Zvadaro, zviratidzo zvine chokuita nekushayikwa kwemasero machena eropa (kusagadzikana kwezvirwere), uye pakupedzisira, kushaya maplatelet eropa (coagulation disorders).

Icho chimiro chisingawanzoitiki cheanemia. Zvichienderana nenyaya yacho, inowanikwa kana kugarwa nhaka. Chirwere ichi chinogona kuonekwa kamwe kamwe uye kwenguva pfupi kana kuva chisingaperi. Pane imwe nguva inenge ichiuraya, aplastic anemia ikozvino inorapwa zviri nani. Zvisinei, kana rikasarapwa nekukasira, rinotonyanya kuipa zvokonzera rufu. Varwere vanenge vanyatsorapwa vanowanzoita zvimwe zvirwere gare gare, kusanganisira gomarara.

Chirwere ichi chinogona kuitika pazera ripi neripi uye chinobata varume nevakadzi (asi kazhinji kacho chakanyanya kuoma muvarume). Inoratidzika kuva yakawanda muAsia kupfuura muUnited States kana Europe.

Zvinokonzera

Mune 70% kusvika 80% yematambudziko6, chirwere chacho hachina chikonzero chinozivikanwa. Zvinozonzi ndeyekutanga kana idiopathic aplastic anemia. Zvikasadaro, hezvino zvinhu zvinogona kukonzera kuitika kwayo:

- Hepatitis (5%)

– Mishonga (6%)

  • Sels d'or
  • Sulfamidés
  • yakachlorichen
  • Non-steroidal anti-inflammatory drugs
  • Anti thyroid mishonga (inoshandiswa mu hyperthyroidism)
  • Phenothiazines
  • Penicillamine
  • Makomborero

- Muchetura (3%)

  • Benzene
  • Canthaxanthine

- Chirwere chechishanu - "tsoka-ruoko-muromo" (parvovirus B15)

-Kubata pamuviri (1%)

- Zvimwe zvisingawanzo zviitiko

Zvakakosha kusiyanisa plastiki anemia kubva kune dzimwe zvirwere zvakafanana nayo. Chokwadi, chirwere ichi chakasiyana neanemias inowanikwa mune mamwe macancer uye kurapwa kwavo.

Kune imwe nhaka yeaplastic anemia inonzi "Fanconi anemia". Pamusoro pekutambura neaplastic anemia, vanhu vane chirwere ichi chisingawanikwe vapfupi pane avhareji uye vane hurema hwakasiyana hwekuzvarwa. Kazhinji, vanoonekwa vasati vasvika makore gumi nemaviri uye vazhinji havasvike pakukura.

Zviratidzo zvechirwere

  • Izvo zvakabatanidzwa kune yakaderera mwero wemasero matsvuku eropa: ruvara rwakacheneruka, kuneta, kushaya simba, dzungu, kukurumidza kurova kwemoyo.
  • Avo vanobatanidzwa kune yakaderera mwero wemasero machena eropa: kuwedzera kubatwa nehutachiona.
  • Idzo dzine hukama nehuwandu hwemaplatelet eropa: ganda rinoputika nyore nyore, kubuda ropa kusina kujairika kubva mumazamu, mhino, chibereko kana gastrointestinal system.

Vanhu vari panjodzi

  • Chirwere ichi chinogona kuoneka pazera ripi zvaro, asi kazhinji kacho chinoonekwa muvana, vanhu vakuru vanenge makore makumi matatu uye vanhu vanopfuura makumi matanhatu.
  • Panogona kunge paine genetic predisposition senge nyaya yeFanconi anemia.

Zvinhu zvinotyisa

Aplastic anemia chirwere chisingawanzoitiki. Vanhu vanotarisana nezvikonzero zvakasiyana-siyana zvechirwere (ona Zvikonzero zviri pamusoro) vanowedzera njodzi yavo yekuchikudziridza, kune zvakasiyana-siyana.

-Kugara kwenguva refu kune zvimwe zvigadzirwa zvine muchetura kana nemwaranzi.

– Kushandisa mimwe mishonga.

- Mamwe mamiriro ezvinhu emuviri: zvirwere (leukemia, lupus), zvirwere (hepatitis A, B, uye C, infectious mononucleosis, dengue), pamuviri (kazhinji kashoma).

dziviriro

Kudzivirira kuratidzwa kwenguva refu kune chepfu kana zvinodhaka zvataurwa pamusoro inzira yekuzvidzivirira nguva dzese - uye kwete kungodzivirira aplastic anemia. Zvisinei, muzviitiko zvakawanda, kutanga kwekutanga kwekupedzisira hakugoni kudziviswa. Kune rumwe rutivi, kana tichiziva kwakabva anemia, zvinokwanisika kudzivirira kudzoka kwayo nekudzivisa kuratidzwa kune chimwe kana chimwe chezvinhu zvinotevera kana zvichibatanidzwa:

- zvinhu zvine chepfu;

- mishonga ine ngozi yakawanda;

-mwaranzi.

Muchiitiko cheaplastic anemia nekuda kwehepatitis, mubvunzo wekushandisa matanho anokurudzirwa kudzivirira marudzi akasiyana ehepatitis. Ona Hepatitis sheet.

Mune yakanyanya aplastic anemia, chiremba dzimwe nguva anorayira mishonga inorwisa mabhakitiriya kudzivirira zvirwere zvebhakitiriya.

Kurapwa

Chirwere chacho hachiwanzoitiki uye chine mikana yakawanda yematambudziko. Kuchengetwa kunozoitwa nachiremba anoona nezvemumunda, nguva zhinji aine timu ine hunyanzvi hwakasiyana-siyana uye munzvimbo ine hunyanzvi.

  • Pakutanga, zvichave zvakakodzera kumisa kutora zvinodhaka zvinogona kukonzera anemia.
  • Mishonga inorwisa mabhakitiriya inozodiwa pakudzivirira uye kurapwa kwechero hutachiona.
  • Iko kusanganiswa kweanti-thymocyte globulins kwemazuva mashanu, cortisone uye cyclosporin inogona, mune dzimwe nguva, kukonzera kuregererwa kwechirwere.7.

Iko kusanganiswa kweanti-thymocyte globulins kwemazuva mashanu, cortisone uye cyclosporine mune dzimwe nguva inogona kukonzera kuregererwa kwechirwere.

Kutarisirwa kwakakosha. Kune vanhu vane aplastic anemia, mamwe matanho ekuzvidzivirira anodiwa muhupenyu hwezuva nezuva:

– Zvidzivirire kubva kuzvirwere. Zvakakosha kugeza maoko ako nguva zhinji nesipo inouraya utachiona uye kuti usasangana nevanhu vanorwara.

– Shaura nebadza remagetsi kwete blade kudzivirira kucheka. Sezvo aplastic anemia inobatanidzwa nehuwandu hwemaplatelet eropa, ropa rinoputika zvishoma uye kurasikirwa kweropa kunofanira kudziviswa zvakanyanya sezvinobvira.

– Kuda mabhurasho emazino ane bristles akapfava.

-Rega kudzidzira mitambo yekusangana. Nokuda kwezvikonzero zvakafanana nezvakataurwa pamusoro apa, zvakakosha kudzivisa chero chiitiko chekurasikirwa kweropa, uye naizvozvo kukuvara.

-Nzvenga kuita maekisesaizi akanyanya. Kune rumwe rutivi, kunyange kurovedza muviri kwakareruka kunogona kukonzera kuneta. Kune rumwe rutivi, muchiitiko chenguva refu yeanemia, zvakakosha kuchengetedza mwoyo. Izvi zvinofanirwa kushanda zvakanyanya nekuda kwekushomeka kwekutakura okisijeni kwakabatana neanemia.

Maonero achiremba

Sechikamu chemaitiro ayo emhando, Passeportsanté.net inokukoka iwe kuti uwane maonero enyanzvi yehutano. Dr Dominic Larose, chiremba wekukurumidzira, anokupa maonero ake pamusoro aplastic kupererwa neropa :

Iyi inguva isingawanzoitiki zvakanyanya iyo iwe uchafanirwa kuonana nachiremba nyanzvi kuti uwane kurapwa kwakakodzera. Vazhinji varapi vese vanozoona nyaya imwe chete mubasa ravo, kana zvachose.

Dr Dominic Larose, MD

 

Nzira dzekuwedzera

Iko hakuna kurapwa kwechisikigo kwakanyatso kuve nyaya yezvidzidzo zvakakomba munyaya yeaplastic anemia.

Maererano neAplastic Anemia & MDS International Foundation, kushandiswa kwemishonga yemakwenzi uye mavhitaminzi kwaigona kuwedzera chirwere uye kukanganisa kugadzirisa. Zvisinei, anokurudzira a Kudya zvine hutano kugadzirisa kugadzirwa kweropa.1

Zvinokurudzirwawo kujoina a boka rekutsigira.

varipo

Kanadha

Aplastic Anemia uye Myelodysplasia Association yeCanada

Iyi saiti inopa rutsigiro uye ruzivo kuvarwere nemhuri. Muchirungu chete.

www.amamac.ca

 

nyika dzakabatana

Aplastic Anemia & MDS International Foundation

Nzvimbo iyi yekuAmerica ine basa repasi rose inotaura mitauro yakawanda uye inofanira kukurumidza kusanganisira chikamu muFrench.

www.aplastic.org

Nhoroondo ye Fanconi Anemia Research Fund, Inc

Nzvimbo iyi yechirungu yakaitirwa vanhu vane Fanconi anemia nemhuri dzavo. Kunyanya, inopa mukana kune bhuku rePDF rakanzi "Fanconi Anemia: Bhuku reMhuri neVarapi Vavo".

www.fanconi.org

 

 

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