Arthrogrypose

Arthrogryposis chirwere chekuzvarwa chinoguma nekuoma kwemajoini. Iyo yakawanda yekufamba saka inogumira. Majoint contractures ane chekuita nechirwere ichi anokura muchibereko uye zviratidzo zviripo kubva pakuzvarwa.

Majoini ese anogona kukanganiswa kana zvimwe chete: mitezo, thorax, musana kana temporomaxillary (shaya).

Kuongororwa kwepamuviri kwakaoma. Inogona kuitwa kana amai vachinzwa kuderera kwekufamba kwe fetus. Kuongororwa kunoitwa pakuzvarwa mushure mekuongorora kwekiriniki uye x-rays. 

Zvikonzero zve arthrogryposis hazvizivikanwe parizvino.

Arthrogryposis, chii ichocho?

Arthrogryposis chirwere chekuzvarwa chinoguma nekuoma kwemajoini. Iyo yakawanda yekufamba saka inogumira. Majoint contractures ane chekuita nechirwere ichi anokura muchibereko uye zviratidzo zviripo kubva pakuzvarwa.

Majoini ese anogona kukanganiswa kana zvimwe chete: mitezo, thorax, musana kana temporomaxillary (shaya).

Kuongororwa kwepamuviri kwakaoma. Inogona kuitwa kana amai vachinzwa kuderera kwekufamba kwe fetus. Kuongororwa kunoitwa pakuzvarwa mushure mekuongorora kwekiriniki uye x-rays. 

Zvikonzero zve arthrogryposis hazvizivikanwe parizvino.

Zviratidzo zve arthrogryposis

Tinogona kusiyanisa akati wandei mafomu arthrogryposis:

Arthrogryposis Multiple Congenital (MCA)

Ndiyo fomu inowanzosangana nayo, pahurongwa hwekuzvarwa vatatu pagumi. 

Inobata mitezo ina yese mu45% yezviitiko, chete makumbo ezasi mu45% yezviitiko uye chete makumbo epamusoro mu10% yematambudziko.

Muzviitiko zvakawanda majoini anokanganisa symmetrically.

Vanenge 10% yevarwere vane abdominal abnomalities nekuda kwekusagadzikana kwemhasuru kuumbwa.

Zvimwe arthrogryposes

Mazhinji fetal mamiriro, genetic kana malformative syndromes inokonzera kuoma kwejoints. Kazhinji kazhinji kune kusagadzikana kwehuropi, musana uye viscera. Zvimwe zvinotungamirira kukurasikirwa kukuru kwekuzvitonga uye zvinoisa upenyu pangozi. 

  • Hecht syndrome kana trismus-pseudo camptodactyly: inobatanidza kuomerwa pakuvhura muromo, kuremara pakuwedzera zvigunwe uye wrist uye equine kana convex varus club tsoka. 
  • Freeman-Shedon kana cranio-carpo-tarsal syndrome, inozivikanwawo semucheche anoridza muridzo: tinocherekedza hunhu hune muromo mudiki, mhuno diki, mapapiro asina kugadzirwa emhino uye epicanthus (kupeta kweganda muchimiro che hafu-mwedzi pakona yemukati yeziso).
  • Moebius syndrome: inosanganisira clubfoot, kuremara kweminwe, uye kuremara kwechiso.

Mishonga yeArthrogryposis

Mishonga haina chinangwa chekurapa chiratidzo asi kupa iyo yakanakisa kuita yemajoini. Vanoenderana nerudzi uye dhigirii rearthrogryposis. Zvichienderana nenyaya, inogona kukurudzirwa:

  • Kugadzirisa kunoshanda kugadzirisa kuremara. Pakarepo kugadzirisa, kufamba kuduku kuchave kwakaganhurirwa.
  • Physiotherapy.
  • Kuvhiya kuvhiyiwa: kunyanya munyaya yegumbo retsoka, chiuno chakatsemuka, kugadziriswa kweaxis yegumbo, kureba kwematendon kana kutamiswa kwemisumbu.
  • Kushandiswa kweorthopedic corset munyaya yekuremara kwemusana.

Tsika yemitambo haina kurambidzwa uye inofanirwa kusarudzwa zvinoenderana nekugona kwemurwere.

Kushanduka kweArthrogryposis

Kuoma kwemajoini hakuiti zvakanyanya mushure mekuzvarwa. Zvisinei, panguva yekukura, kusashandisa kwemakumbo kana kurema kunorema kunogona kutungamirira kuhutano hwakanyanya hwemapfupa.

Simba retsandanyama rinongokudziridzwa zvishoma. Saka zvinogoneka kuti haichakwani pane mamwe mitezo kumurwere mukuru.

Iyi syndrome inogona kunyanya kuremadza muzviitiko zviviri:

  • Kana kurwiswa kwenhengo dzezasi kuchida kuti mudziyo umire wakatwasuka. Izvi zvinoda kuti munhu akwanise kuzviisa ega kuti azvitonge uye nekudaro ave nekushandisa kunenge kwakajairika kwemakumbo ake epamusoro. Kushandiswa uku kunofanirawo kunge kwakazara kana, kufamba-famba, rubatsiro rwemazimbe rinodikanwa.
  • Apo kubudirira kwemakumbo mana kunoda kushandiswa kwemagetsi emagetsi uye kushandiswa kwemunhu wechitatu.

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