Little's syndrome izwi rinofanana nerekuti infantile spastic diplegia.

Infantile spastic diplegia ndiyo inonyanya kuzivikanwa cerebral palsy. Iyo inoratidzirwa nekuoma kwemisumbu munyaya yakakanganiswa, kunyanya mumakumbo uye zvishoma mumaoko uye chiso. Hyperactivity mumatendon emakumbo inoonekwawo mune iyi pathology.

Uku kuoma kwemhasuru mumakumbo emunhu abatwa kunokonzera kusawirirana mukufamba kwemakumbo nemaoko.

Muvana vane Little's syndrome, mutauro uye njere zvinowanzoitika. (1)

Iyi cerebral diplegia kazhinji inotanga mucheche kana vana vadiki.

Vanhu vane chirwere ichi vane kuwedzera kwetsandanyama toni inotungamira kune tsandanyama spasticity. Ichi chiitiko chepamusoro uye chisingaperi chemhasuru toni yemamhasuru pakuzorora. Kuwedzeredza pfungwa kunowanzova mugumisiro. Iyi tsandanyama spasticity inonyanya kukanganisa tsandanyama dzemakumbo. Misumbu yemaoko, kune chikamu chavo, haina kukanganiswa kana kusakanganiswa.

Zvimwe zviratidzo zvinogona kuva zvakakosha zvechirwere. Iyi ndiyo nyaya, semuenzaniso, yekufamba pamusoro pezvigunwe kana kuti discordant walk.

Izvi zvisina kujairika muzwi retsandanyama mhedzisiro yekukanganisika mutsinga dzeuropi kana kukura kwavo kusiri kujairika.

Zvishoma zvinozivikanwa pamusoro pechikonzero chaicho chechirwere chetsinga ichi. Kunyange zvakadaro, vamwe vatsvakurudzi vakafungidzira kuti kune hukama nekuchinja kwemavara okugara nhaka, kukanganisa kweuropi, utachiona kana fivha muna amai panguva yavanenge vaine pamuviri kana kuti tsaona pavanenge vachisununguka kana kuti vachangozvarwa. kuberekwa. (3)

Kusvika iye zvino, hapana mishonga yekurapa yechirwere ichi. Mukuwedzera, kune dzimwe nzira dzemishonga dziripo zvichienderana nezviratidzo, zviratidzo uye kuoma kwechirwere. (3)

Kune marudzi akasiyana ekuoma kwechirwere.

Zviratidzo zveLittle's syndrome saka zvakasiyana kubva kune mumwe murwere kuenda kune mumwe.

Mumamiriro ezvinhu ecerebral palsy nekuda kwekukanganiswa kwetsinga, zviratidzo zvinoonekwa kare kare muhuduku. Zviratidzo zvekiriniki zvinosanganiswa kukanganisa kwemhasuru (kunyanya mumakumbo) izvo zvinokanganisa kutonga kwetsandanyama uye kurongeka.

Mwana ari kutambura nechirwere ichi anopa tsandanyama toni yakakwirira kupfuura yakajairwa uye yakawedzera reflexes (mhedzisiro yekukura kwe spasticity).

Zvimwe zviratidzo zvinogonawo kuva zviratidzo zvekukura kwevacheche spastic diplegia. Kunyanya zviratidzo zvinoratidza kunonoka muunyanzvi hwemotokari yemwana, kufamba kwakamira pazvigunwe, kufamba kweasymmetrical, nezvimwewo.

Muzviitiko zvisingawanzoitiki, zviratidzo izvi zvinoshanduka pamusoro pehupenyu hwomunhu. Zvisinei, kazhinji izvi hazvishanduke nenzira isina kunaka. (3)

Mukuwedzera kune izvi zviratidzo zveunyanzvi hwemotokari, zvimwe zvisizvo zvingave zvine chokuita nechirwere mune dzimwe nguva: (3)

- hurema hwepfungwa;

- kudzidza matambudziko;

- kugwinha;

- kuderera kwekukura;

- kukanganisa mumusana;

- osteoarthritis (kana arthritis);

- kusaona zvakanaka;

- kurasikirwa nekunzwa;

- matambudziko emutauro;

- kurasikirwa kwekutonga urinary;

– tsandanyama contractures.

Infantile spastic diplegia (kana kuti Little's syndrome) chirwere checerebral palsy chinokonzerwa nekusakura zvakanaka kwechikamu cheuropi chinodzora hunyanzvi hwemotokari.

 Uku kukanganisa mukukura kweuropi kunogona kukonzerwa vasati vazvarwa, panguva, kana kuti vachangozvarwa.

Muzviitiko zvakawanda, chikonzero chaicho chekukura kwechirwere hachizivikanwi.

Zvisinei, fungidziro dzakaitwa, dzakadai se: (1)

- genetic abnormalities;

- congenital malformations muuropi;

- kuvapo kwezvirwere kana fivha muna amai;

- kukuvara kwe fetal;

- nezvimwewo.

Mamwe mavambo echirwere akajekeswawo: (1)

– intracranial kubuda ropa izvo zvinogona kukanganisa kutenderera kweropa muuropi kana kukonzera kuputika kwetsinga dzeropa. Kubuda ropa uku kunowanzokonzerwa nekuvhunduka kwe "fetus" kana kuumbwa kwegwamba reropa mubeche. High blood pressure kana kukura kwezvirwere muamai panguva yekuzvitakura kunogonawo kuva chikonzero;

- kuderera kweokisijeni muuropi, zvichiita kuti cerebral asphyxia. Ichi chiitiko chinowanzoitika mushure mekusununguka kwakanyanya. Kuvhiringidzwa kana kuderedzwa kweokisijeni saka kunotungamirira kukukuvadza kukuru kumwana: inonzi hypoxic ischemic encephalopathy (EHI). Iyo yekupedzisira inotsanangurwa nekuparadzwa kwehuropi tishu. Kusiyana nezvakaitika kare, hypoxic ischemic encephalopathy inogona kuva mugumisiro we hypotension muna amai. Kutsemuka kwechibereko, kupatsanurwa kwebepa, kusanzwisisika kunokanganisa rukuvhute kana kukuvadzwa kwemusoro panguva yekusununguka kunogonawo kuva chikonzero;

- kusagadzikana muchikamu chichena checerebral cortex (chikamu cheuropi chinokonzera kutumira zviratidzo kubva muuropi kuenda kumuviri wose) zvakare chimwe chikonzero chekukura kwechirwere;

- kukura kusina kujairika kwehuropi, mhedzisiro yekuvhiringidzwa kwemaitiro akajairika ekukura kwayo. Ichi chiitiko chakabatana nekuchinja kwemajini encoding kuumbwa kwecerebral cortex. Utachiona, kuvapo kwefivha inodzokororwa, kushungurudzika kana mararamiro asina kunaka panguva yekuzvitakura kunogona kuve imwe njodzi yekukura kwehuropi husina kujairika.

Izvo zvinonyanya kuisa njodzi zvinokonzeresa Little's syndrome ndezvi: (1)

- kusagadzikana mumazinga emamwe majini anonzi ari kufanotungamira;

- congenital malformations muuropi;

- kukura kwezvirwere uye kupisa kwakanyanya muna amai;

- intracranial maronda;

- kuderera kweokisijeni muuropi;

-kukanganisa kwekukura kwecerebral cortex.

Mamwe mamiriro ekurapa anogona kunge ari nyaya yengozi yakawedzera yekukura cerebral palsy muvana: (3)

- kuberekwa nguva isati yakwana;

- kurema kwakareruka pakuzvarwa;

- utachiona kana kupisa kwakanyanya panguva yekuzvitakura;

- mimba dzakawanda (mapatya, katatu, nezvimwewo);

- kusapindirana kweropa pakati paamai nemwana;

- kukanganisa kwethyroid, kuremara kwenjere, mapuroteni akawandisa muweti kana kugwinha muna amai;

- kuberekwa kwebhurugwa;

- matambudziko panguva yekusununguka;

- yakaderera Apgar index (index yehutano hwemucheche kubva pakuberekwa);

- jaundice yemwana achangoberekwa.

Kuongororwa kwevacheche spastic diplegia kunofanira kuitwa nokukurumidza mushure mekuberekwa kwemwana kuitira kugara zvakanaka kwemwana nemhuri yake. (4)

Kunyatso ongorora chirwere kunofanirawo kuitwa. Izvi zvinoreva kukudziridza kutarisa kwemwana panguva yekukura kwake uye kukura. Kana kutevera uku kwemwana kukava nemigumisiro inoshungurudza, kuongororwa kwekuongorora kwekukura kunogoneka.

Kuongororwa kwekukura kwemwana uku kunoguma nemiedzo yekuongorora kunonoka kungaita mukukura kwemwana, sekunonoka kwehunyanzvi hwemotokari kana kufamba.

Muchiitiko apo migumisiro yechikamu chechipiri chekuongorora ichi chinowanikwa chakakosha, chiremba anogona kuzoenderera mberi nekuongorora kune kuongororwa kwehutano hwehutano.

Chinangwa chechikamu chekukura kwechirwere chekurapa ndechekuratidza kusaenzana kwakanyanya mukukura kwemwana.

Kuongororwa kwekurapa uku kunosanganisira kumwe kuedzwa kwekuziva kusaenzana kwechirwere, ndeiyi: (3)

- kuongorora ropa;

- cranial scanner;

- MRI yemusoro;

- electrencephalogram (EEG);

- electromyography.

Panyaya yekurapa, parizvino hapana mushonga wechirwere ichi.

Zvisinei, marapiro anogona kuvandudza mararamiro evarwere. Mishonga iyi inofanirwa kunyorerwa nekukurumidza mushure mekuonekwa kwechirwere.

Mishonga inonyanyozivikanwa ndeye zvinodhaka, kuvhiyiwa, kutsemuka, uye nemuviri (physiotherapy) uye nemutauro (speech therapy) kurapwa.

Zviyamuro zvekuchikoro zvinogona kupihwa kune vanhu vane chirwere ichi.

Kurongeka kwakakosha kwevarwere vane chirwere ichi kunosiyana zvakanyanya zvichienderana nezviratidzo uye zviratidzo zviripo mumunhu.

Zvechokwadi, zvimwe zvidzidzo zvinobatwa nenzira ine mwero (hapana muganhu mukufamba kwavo, rusununguko, nezvimwewo) uye zvimwe zvakanyanya (kusakwanisa kuita mamwe mafambiro pasina rubatsiro, nezvimwewo) (3).