Kurapa, kutarisira, kudzivirira hemochromatosis

Kurapa, kutarisira, kudzivirira hemochromatosis

Kurapa kwehemochromatosis kunobva pane kudeura ropa (inonziwo phlebotomies). Vanovavarira kudzikisa chiyero chesimbi muropa uye kuderedza iron deposits mumuviri pasina kukonzera iron kushomeka anemia.

Maitirwo acho akafanana neanoitwa pakupa ropa. Inokurudzirwa kunwa mvura mushure mekubuda ropa.

Iyo iri nyore, isingadhuri uye inoshanda kurapwa, kazhinji inoitwa pakati pe4 ne6 kanomwe pagore, pasina kukanganisa kwehupenyu hwemurwere, kunyanya sezvo kubuda ropa kunogona kuitwa kumba.

Chiremba anotsanangura huwandu hweropa rinofanira kutorwa anowanzoonekwa mumurwere tichifunga nezvezera rake, uremu uye urefu. Pakutanga, kubuda ropa kwevhiki nevhiki kunodiwa uye kunochengetwa chero bedzi iron yakawandisa ichionekwa. Apo chiyero cheferritin muropa chinowira pasi pe 50 μg / L, inoitwa pamwedzi kana kota semhosva inogona kunge iri kuchengetedza chiyero cheferritin muropa pasi pe50 μg / L. Vachachengetwa kwehupenyu hwose.

Mushonga uyu haurape chirwere.

Muvakadzi vane pamuviri, kubuda ropa hakuitike panguva yose yekuzvitakura. Iron supplementation haifaniri.

Zvimwe zvinetso zvechirwere (cirrhosis, mwoyo kusakundikana kana chirwere cheshuga) inyaya yekurapa chaiyo.


Cherechedza kuti hapana kudya kunogona kutsiva kurapwa nekubuda ropa. Murwere anokurudzirwa kutevera kudya kwemaitiro uye kuderedza kunwa doro.

 

Zvakanakira kurapwa

Nekurapa, kuneta kunowanzoonekwa kune varwere vane hemochromatosis kunoderedzwa. Kunyanya, apo kurapwa kunotanga kare, kunobatsira kudzivisa matambudziko makuru echirwere (kukuvadza kumwoyo, chiropa uye pancreas) uye nokudaro kurebesa hupenyu hwevarwere.

Hapana shanduko mumaitiro evarwere inofanirwa kutariswa muhemochromatosis kunze kwemitemo yehutsanana hwehupenyu iyo inosanganisira kudya kwakajairika uye kuderedzwa kwezvinwiwa zvinodhaka kana kuwandisa kwaimboitwa.

Varwere vanotariswa mumadhipatimendi ehepato-gastroenterology. Mune vanhu vari pangozi, kubvunzurudza kwemajini kunoratidzwa zvachose kuitira kuti vaone chirwere chacho nokukurumidza uye kutora matanho anodiwa ekurapa.

MuFrance, mafomu epamusoro ehemochromatosis ndeimwe ye30 yenguva refu mamiriro (ALD 30).

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