Dermatomyositis chirwere chisingaperi chinokanganisa ganda uye tsandanyama. Icho chirwere che autoimmune icho chisati chazivikanwa, chakaiswa muboka reidiopathic inflammatory myopathies, pamwe chete nemuenzaniso polymyositis. Iyo pathology inoshanduka kwemakore ine fungidziro yakanaka, mukusavapo kwematambudziko akakomba, asi inogona kukanganisa hunyanzvi hwemotokari yemurwere. Zvinofungidzirwa kuti 1 mu50 kusvika ku000 mu1 vanhu vanorarama nedermatomyositis (kupararira kwayo) uye kuti nhamba yezvirwere zvitsva gore negore i10 kusvika ku000 pamamiriyoni evanhu (chiitiko chayo). (1)

Zviratidzo zvedermatomyositis zvakafanana kana zvakafanana kune izvo zvinosanganiswa nemamwe myopathies inoputika: maronda eganda, kurwadziwa kwemisumbu uye kushaya simba. Asi zvinhu zvakati wandei zvinoita kuti zvikwanise kusiyanisa dermatomyositis kubva kune mamwe anopisa myopathies:

• Zvigamba zvitsvuku zvakatsvuka uye zvakatsvuka kumeso, mutsipa nemapfudzi zvinowanzova zviratidzo zvekutanga zvekiriniki. Izvo zvinogona kukanganisa maziso, nenzira yegirazi, hunhu.
• Misumbu inobatwa nesymmetrically, kutanga kubva pahunde (abdominals, mutsipa, trapezius ...) isati yasvika, mune dzimwe nguva, maoko nemakumbo.
• Mukana wepamusoro wekubatanidzwa nekenza. Gomarara iri rinowanzotanga mumwedzi kana makore mushure mechirwere, asi dzimwe nguva panongotanga zviratidzo zvekutanga (zvinoitikawo pamberi pavo). Kazhinji kazhinji igomarara rezamu kana maovaries kuvakadzi uye remapapu, prostate nema testes kuvarume. Zvitubu hazvibvumirani nezve njodzi kune vanhu vane dermatomyositis yekuva nekenza (10-15% kune vamwe, chikamu chimwe muzvitatu kune vamwe). Neraki, izvi hazvishande kune chimiro chechidiki chechirwere.

Iyo MRI uye tsandanyama biopsy inosimbisa kana kuramba kuongororwa.

Yeuka kuti dermatomyositis chirwere cheboka reidiopathic inflammatory myopathies. Chirevo chekuti "idiopathic" kureva kuti kwaakabva hakuzivikanwe. Kusvika iye zvino, naizvozvo, hapana chikonzero kana nzira chaiyo yechirwere ichi inozivikanwa. Zvingangoitika kubva mukusanganiswa kwemajini uye zvakatipoteredza.

Nekudaro, isu tinoziva kuti chirwere che autoimmune, ndiko kuti kukonzeresa kukanganisa kwedziviriro yekudzivirira, autoantibodies inopokana nemuviri, mune iyi kesi ichipokana nemamwe masero emhasuru neganda. Cherechedza, zvisinei, kuti havasi vanhu vose vane dermatomyositis vanobudisa izvi autoantibodies. Zvinodhaka zvinogonawo kukonzeresa, sezvinoita mavhairasi. (1)

Vakadzi vanobatwa nedermatomyositis kakawanda kupfuura varume, kanenge kaviri. Izvi zvinowanzoitika nezvirwere zve autoimmune, pasina kuziva chikonzero. Chirwere ichi chinogona kuoneka pazera ripi neripi, asi zvinoonekwa kuti zvinonyanya kuoneka pakati pemakore 50 ne60. Nezve juvenile dermatomyositis, inowanzova pakati pemakore mashanu ne5 ekuberekwa kuti inoratidzika. Zvinofanira kusimbiswa kuti chirwere ichi hachina kutapuriranwa kana kugarwa nhaka.

Mukushaikwa kwekukwanisa kuita pane (zvisingazivikanwe) zvikonzero zvechirwere, marapirwo edermatomyositis anovavarira kuderedza / kubvisa kuzvimba nekupa corticosteroids (corticosteroid therapy), pamwe nekurwisa kugadzirwa kweautoantibodies kune iyo nzira. immunomodulatory kana immunosuppressive zvinodhaka.

Mishonga iyi inoita kuti zvikwanise kudzikamisa marwadzo emhasuru uye kukuvadzwa, asi matambudziko anogona kumuka muchiitiko chegomarara uye kusagadzikana kwakasiyana (moyo, pulmonary, nezvimwewo). Juvenile dermatomyositis inogona kukonzera matambudziko makuru ekugaya muvana.

Varwere vanofanira kuchengetedza ganda ravo kubva kuzuva reUV rays, iyo inogona kuwedzera maronda eganda, nenzira yekufukidza zvipfeko uye / kana kudzivirira kwakasimba kwezuva. Pakangotanga kuongororwa, murwere anofanirwa kugara achiongororwa gomarara rine chekuita nechirwere ichi.