General tsananguro yechirwere
Iyo isingawanzo kuwanikwa nhaka yeropa kusagadzikana umo matambudziko ekuvhara ropa anoonekwa.
Mhando dzehemophilia
Hemophilia chirwere chemajini umo rimwe geni pane X chromosome inochinja. Zvichienderana nekuti geni rashanduka sei, rudzi rwechirwere rwakaparadzaniswa. Hemophilia ndeyemhando nhatu: A, B, C.
- Type A - hapana yakakosha mapuroteni muropa: antihemophilic globulin, factor VIII yekugwamba kweropa. Iyi geni kuremara inowanikwa mu85% yevarwere uye inoonekwa seyakajairika.
- Type B - chinhu IX hachishande zvakakwana, nekuda kwekuti maitiro ekuumbwa kwepuragi yechipiri yekuvhara yakavhiringidzwa.
- Nyorai C - hemophilia yerudzi urwu inoitika nekuda kwekukwana huwandu hwe XI coagulation factor. Rudzi C mhando isingawanzoitika, iyo yainyanya kubata maAshkenazi maJuda. Vakadzi nevarume vanogona kurwara nazvo. Parizvino, mhando iyi yabviswa muchikamu nekuda kwekuti zviratidzo zvaro zvakasiyana zvakanyanya kubva kune maviri ekutanga marudzi.
Zvinokonzera chirwere
Chikonzero chikuru chekusimudzira hemophilia chinotorwa senhaka.
Mhosva hadziwanzoitika "pakarepo hemophilia“. Iye anongoerekana aonekwa, kunyange mhuri yakanga isina chirwere ichi. Shure kwaizvozvo, iyi fomu yehemophilia inopfuudzwa patsika - padanho rekuberekwa. Nyanzvi dzezvechiremba hadzisati dzaziva zvikonzero chaizvo zvekukura kwechirwere. Ivo vanotenda kuti ichi chitsva geni shanduko.
Iko mukana wekugara nhaka hemophilia
Kazhinji varume vanotambura nechirwere ichi. Chirwere ichi chinopfuudzwa kune murume pabonde nenzira yakawandisa (yakabatana neX chromosome). Kana mwanakomana akagara nhaka yechikadzi X - chromosome, haapi hemophilia. Vakadzi vanopihwa basa re "conductor" kana mutakuri, asi panogona kunge paine kusarudzika. Kana baba vachirwara nehemophilia, uye amai vari mutakuri, vabereki vakadaro vanogona kunge vaine musikana ari kutambura nechirwere ichi. Pakazara, angangoita makumi matanhatu emakesi akanyoreswa mupasi umo vasikana vakatambura hemophilia, uye vaive vasiri vatakuri.
Pane matatu akasiyana ekuparadzira hemophilia
- 1 Amai ndivo vanotakura geni, asi baba murume ane hutano. Muchiitiko ichi, zvibodzwa zvina zvinogoneka, pamwe mukana we4%. Mwanakomana ane hutano kana mwanasikana ane hutano, mwanakomana anorwara kana mwanasikana anotakura anogona kuzvarwa.
- 2 Amai vane hutano, baba vanorwara nehemophilia. Mune ino mamiriro, vese vanakomana vachave vakagwinya, uye vanasikana vese vanozove vatakuri.
- 3 Amai ndivo vanotakura geni, uye baba vari kurwara. Mune izvi zvakasiyana, panogona kuve nezvibodzwa zvina: mwanakomana ane hutano, mwanasikana anorwara, mwanakomana anorwara, kana mwanasikana anotakura. Mhedzisiro yega yega ine masimba akaenzana.
Zviratidzo zvehemophilia
Mune hemophilia, kubuda ropa kwakanyanyisa kunoonekwa, kunoitika nguva nenguva nenzvimbo dzakasiyana panguva dzekukuvara kwakasiyana siyana, nzira dzekurapa (kunyanya majekiseni epamuviri uye kupindira kwekuvhiya), uye panobviswa mazino.
Gamu kana kubuda ropa kunonetsa kumisa. Uyezve, kubuda ropa kungangoitika.
Nekukuvadzwa kuduku uye kupwanya, yakakura hematoma inoumbwa.
Chinhu chikuru chehemophilia ndiko kubuda kweropa mukati - articular - hemarthrosis. Kana zvikaonekwa mumubatanidzwa, kufamba kunokanganisa, kuzvimba kunoitika. Zvese izvi zvinofambidzana nekurwadziwa kwakanyanya. Mushure mekutanga kubuda ropa kwakadaro, iro ropa riri mujoini rinosungunuka roga uye mashandiro ejojo anodzoreredzwa. Asi nekudzokorora, kugwinha kunoita pajoini capsule uye shwashwa, iyo yakafukidzwa neyakaungana matishu. Ankylosis inokura nekuda kwemaitiro akadaro.
Chimwe chiratidzo chakakosha muhemophilia ndiko kunonoka, kunonoka chimiro chekubuda ropa. Kubuda ropa hakuvhure pakarepo mushure mekukuvara, asi mushure menguva yakati rebei. Izvi imhaka yekuti pakutanga kubuda ropa kwakamiswa nemaplatelet, iwo marongerwo acho asina kuchinjwa. Zvinogona kutora kubva pa6 kusvika kumaawa gumi nemaviri ropa risati ravhurika - zvese zvinoenderana nekukura kwechirwere.
Panogona kunge paine ropa mumurini kana mutsvina. Chiratidzo chakaomesesa uye chinouraya chehemophilia kubuda ropa mumuzongoza kana huropi.
Kune vana, haemophilia inogona kutora nguva yakareba kuti ikure. Izvi zvinoshanda kuvacheche vanoyamwiswa naamai. Chokwadi, mumukaka wemuzamu pane zvakakosha zvinhu zvinotsigira kugona kweropa kuvhara zvakajairika. Naizvozvo, kana amai vachiwedzera kuyamwisa mwana, iwo ekupedzisira zviratidzo zvekutanga zvichaonekwa.
Mafomu ehemophilia
Zvichienderana nekuomarara kwechirwere, 3 mafomu ehemophilia anosiyaniswa.
- RџS•Rё munyoro hemophilia kubuda ropa kunoitika chete panguva yekuvhiyiwa kana mushure mekukuvara zvakanyanya. Muropa, iyo coagulation factor iri mune huwandu hwe5-25%.
- RџS•Rё zvine mwero kosi hemophilia ichibatanidza chinhu muropa iri mune chikamu che1 kusvika ku5%. Zviratidzo zvekutanga zvekiriniki zvinogona kuonekwa vachiri vadiki. Kune iyi fomu, kubuda ropa kunowanikwa mukukuvara zvine mwero, uye nemavanga madiki, mahematoma akakomba anoitika.
- RџS•Rё fomu yakaoma zvirwere, ropa rine coagulation chinhu isingasviki 1%. Muchiitiko ichi, hemophilia inozviratidza mumwedzi yekutanga yehupenyu - panguva yekucheka, kubuda ropa kunovhura, uye pakuedza kwekutanga kufamba, mahematoma akasimba uye akazara anoonekwa (panguva yekukambaira, nekuda kwekukanya kwechinhu chero chipi zvacho kana kudonha).
Varwere vanozivikanwa uye vatakuri vehemophilia
Mambokadzi Victoria anoonekwa seanonyanya kutakura hemophilia munhoroondo. Uyezve, hazvizivikanwe zvakavimbika nekuda kwezvikonzero zvaakave akadaro. Mushure mezvose, zvisati zvaitika, hapana mumhuri akatambura nechirwere ichi. Pane mavhezheni maviri.
Wekutanga anobvuma kuti baba vake vangadai vakave mumwe murume airwara nehemophilia, uye kwete Mutongi weKent Edward Augustus. Asi hapana humbowo hwakanyorwa.
Naizvozvo, yechipiri vhezheni yakaiswa pamberi - Victoria ane shanduko mumageneti ake. Ndokunge, aive ne "otomatiki" chimiro chehemophilia. Uye maererano neyakajairwa mutemo, hemophilia yakagarwa nhaka nemwanakomana wake - Duke weAlbany, Leopold nevamwe vazukuru uye vazukuru.
Hemophilia inonzi chirwere chemadzimambo. Izvi zvinotsanangurwa nenyaya yekuti pakutanga, nekuda kwekuchengetedza zita, michato nehama dzepedyo dzaibvumidzwa. Naizvozvo, mukana wekuve nevana vanorwara kudare wakawedzera zvakanyanya.
Iyo nhema yehemophilia
Iko kune fungidziro yekuti munhu ane hemophilia anogona kubuda ropa kusvika pakufa pane chero kuderera kukuvara paganda. Chirevo ichi hachisi chokwadi, uye kune vanhu vakadaro, kukwenya kuduku uye kucheka hazviunzi ngozi yekufa.
Njodzi kupindira kwekuvhiya, kudhonza mazino, majekiseni uye kubuda kweropa kamwe kamwe mumasumbu nemidzi yeropa, izvo zvinoitika nekuda kwemadziro asina kusimba evascular muvarwere.
Kudya kune hutano kwehemophilia
Nehemophilia, hapana mirau yakasimba yekudya iyo inofanirwa kutevedzwa.
Kuti udzore ropa uye kuvandudza kugwamba, zvakafanira kudya chikafu chine munyu wephosphorus, calcium, mavitamini A, B, C, D. Chinhu chakakosha kupa muviri huwandu hunodiwa hwevhitamini K. Inodaidzwa iyo coagulation (coagulation) vhitamini.
Vitamin K inogona kuwanikwa nekudya sipinashi, lettuce, hanyanisi, karoti, mabhanana, gariki, magaka, matomatisi, mapeya, maapuro, kabichi (kunyanya broccoli, chena kabichi, kolifulawa), mhiripiri inopisa, soya, zai yolk, chizi, mafuta ebhata , oats, topip misoro, celery.
Kuti uvandudze mamiriro eropa, simudza hemoglobin, simbisa madziro emidziyo yeropa uye udzikise cholesterol, zvinofanirwa kusanganisira mukudya chiropa, hove dzakakora, michero yemuchero, nzungu, pomegranate, avocado, beet, cranberry muto, uchi , porridge yebhakkwheat, karoti, maapuro uye majusi eBeet…
Beet muto unofanirwa kudhakwa wakadzvanywa nekaroti kana muto wemaapuro. Kutanga, inofanirwa kuve yakadzvanywa 1 kusvika 1, zvobva zvadzora zvishoma nezvishoma kuwedzera uye kuwedzera kuwanda kweiyo beet muto.
Zvakare, iwe unogona kunwa yakanatswa mvura, girini tii, tii ne currants, viburnum kana raspberries, rosehip decoction.
Chinyakare mushonga wehemophilia
Kuti udzivise kubuda kweropa, varwere vanogona kutora svinu yembeu yemazambiringa, decoctions ye dioecious nettle, yarrow, astragalus, Japan sophora, chikwama chemufudzi, arnica, coriander, muroyi hazel, dandelion mudzi. Izvi zvinomera zvekurapa zvinobatsira kusimbisa madziro emitsipa yeropa, kuwedzera kugwamba kweropa nekuvandudza mhando yeropa.
Iwe unofanirwa kutora asipurini shoma uye mimwe mishonga yekuonda-ropa, iyo inogona kukonzera kubuda ropa.
Chikafu chine njodzi uye chinokuvadza chehemophilia
- chikafu chine mafuta (chine huwandu hwakawanda hwecholesterol, nekuwedzera, mafuta anodzivirira kunwa kwecalcium, uye yakakosha pakuenzanisa kwemaseru);
- yakakangwa, munyu, yakasvuta ndiro (chikafu ichi chine zvinhu zvinoshandura kuumbwa kweropa kwete kuti zvive nani, ndosaka shanduko dzisina kunaka dzichiitika mumuviri wese mune ramangwana);
- doro, inotapira soda, zvinwiwa zvine simba (zvinoparadza uye kushayisa mvura mumasero eropa, ndosaka ropa risingakwanise kubata nemabasa aro);
- chikafu chekukurumidza, mafuta ekubikisa, zvigadzirwa zvinopera, chikafu chekare, chengetedza chikafu chemumagaba, masoseji, masosi uye zvinorungwa, pamwe nekudya zvine zvakasiyana-siyana zvekudya zvinowedzera (izvi "zvigadzirwa" zvinoumba makomisheni anorema ayo masero eropa asingagoni kushandisa kupa muviri wemunhu. , asi ivo pachavo vanogadzira chepfu mumuviri nezvinhu izvi zvinokuvadza zveballast).
Chenjerera!
Iwo manejimendi haatarisiri chero kuyedza kwekushandisa ruzivo rwunopihwa, uye haivimbise kuti harukuvadze iwe pachezvako. Izvo zvinhu hazvigone kushandiswa kupa mushonga uye kugadzirisa chirwere. Nguva dzose bvunza chiremba wako wezvechiremba!