Hyperlaxité

Hyperlaxité

Chii ?

Hyperlaxity yakawandisa majoini mafambiro.

Kuramba uye kusimba kwezvinyama zvemukati zvemuviri zvinodzorwa nemamwe maprotein akabatana. Panyaya yekuchinja mukati memapuroteni aya, kusakwana kune chekuita nenhengo dzemuviri dzinofamba (majoini, tendon, cartilage uye ligaments) zvinobva zvanyanya kukanganiswa, zvichiva panjodzi uye zvisina kusimba uye zvinogona kukonzera maronda. Naizvozvo i articular hyperlaxity.

Iyi hyperlaxity inotungamira kune nyore uye isingarwadze hyper-extension yedzimwe nhengo dzemuviri. Uku kushanduka kwemakumbo ndiwo mhedzisiro yakananga yekusagadzikana kana kunyangwe kusavapo kwemarunda uye dzimwe nguva yefupa fragility.

Iyi pathology inobata zvakanyanya mapendekete, magokora, mawoko, mabvi uye zvigunwe. Hyperlaxity inowanzoitika muhuduku, panguva yekugadzirwa kwekubatanidza tishu.

Mamwe mazita ane chekuita nechirwere ichi, ndeaya: (2)

- hypermobility;

- chirwere chemakumbo akasununguka;

- hyperlaxity syndrome.

Vanhu vane hyperlaxity vanonzwa zvakanyanya uye vane njodzi yakanyanya yekutsemuka uye ligament dislocation panguva ye sprains, strains, nezvimwe.

Nzira dzinoita kuti zvikwanisike kudzikamisa njodzi yematambudziko mumamiriro eiyi pathology, kunyanya:

- maekisesaizi ekusimbisa tsandanyama uye ligament;

- kudzidza "yakajairika siyana" yekufamba kuitira kudzivirira hyper-extensions:

- kuchengetedzwa kwemarunda panguva yekurovedza muviri, uchishandisa padding masisitimu, mabvi mapedhi, nezvimwe.

Kurapa kwechirwere kunosanganisira kubvisa marwadzo uye kusimbisa ligament. Muchirevo chechinyorwa chino, kunyorerwa kwemishonga (makirimu, sprays, nezvimwewo) inowanzobatanidzwa uye inoperekedzwa nekurapa kwekurovedza muviri. (3)

zviratidzo

Hyperlaxity yakawandisa majoini mafambiro.

Kuramba uye kusimba kwezvinyama zvemukati zvemuviri zvinodzorwa nemamwe maprotein akabatana. Panyaya yekuchinja mukati memapuroteni aya, kusakwana kune chekuita nenhengo dzemuviri dzinofamba (majoini, tendon, cartilage uye ligaments) zvinobva zvanyanya kukanganiswa, zvichiva panjodzi uye zvisina kusimba uye zvinogona kukonzera maronda. Naizvozvo i articular hyperlaxity.

Iyi hyperlaxity inotungamira kune nyore uye isingarwadze hyper-extension yedzimwe nhengo dzemuviri. Uku kushanduka kwemakumbo ndiwo mhedzisiro yakananga yekusagadzikana kana kunyangwe kusavapo kwemarunda uye dzimwe nguva yefupa fragility.

Iyi pathology inobata zvakanyanya mapendekete, magokora, mawoko, mabvi uye zvigunwe. Hyperlaxity inowanzoitika muhuduku, panguva yekugadzirwa kwekubatanidza tishu.

Mamwe mazita ane chekuita nechirwere ichi, ndeaya: (2)

- hypermobility;

- chirwere chemakumbo akasununguka;

- hyperlaxity syndrome.

Vanhu vane hyperlaxity vanonzwa zvakanyanya uye vane njodzi yakanyanya yekutsemuka uye ligament dislocation panguva ye sprains, strains, nezvimwe.

Nzira dzinoita kuti zvikwanisike kudzikamisa njodzi yematambudziko mumamiriro eiyi pathology, kunyanya:

- maekisesaizi ekusimbisa tsandanyama uye ligament;

- kudzidza "yakajairika siyana" yekufamba kuitira kudzivirira hyper-extensions:

- kuchengetedzwa kwemarunda panguva yekurovedza muviri, uchishandisa padding masisitimu, mabvi mapedhi, nezvimwe.

Kurapa kwechirwere kunosanganisira kubvisa marwadzo uye kusimbisa ligament. Muchirevo chechinyorwa chino, kunyorerwa kwemishonga (makirimu, sprays, nezvimwewo) inowanzobatanidzwa uye inoperekedzwa nekurapa kwekurovedza muviri. (3)

Kwakatangira chirwere

Zviitiko zvakawanda zve hyperlaxity hazvina hukama kune chero chikonzero chinokonzera. Muchiitiko ichi, ndeye benign hyperlaxity.

Mukuwedzera, iyi pathology inogonawo kubatanidzwa ne:

- kukanganisa muhutano hwemapfupa, chimiro chemapfupa;

- kukanganisa kwezwi uye kuoma kwemhasuru;

- kuvapo kwe hyperlaxity mumhuri.

Mhosva iyi yekupedzisira inoburitsa mukana wekugara nhaka mukutapurirana kwechirwere.

Muzviitiko zvisingawanzoitiki, hyperlaxity inokonzerwa nemamiriro ezvinhu ehutano. Izvi zvinosanganisira: (2)

- Down syndrome, inoratidzwa nekuremara kwenjere;

- cleidocranial dysplasia, inoratidzirwa nekusagadzikana kwakagarwa nhaka mukukura kwemapfupa;

-Ehlers-Danlos syndrome, inoratidzirwa nekusimba kwakakosha kweiyo inobatanidza tishu;

- Marfan Syndrome, inovawo chirwere chinobatanidza;

- Morquio syndrome, chirwere chakagara nhaka chinokanganisa metabolism.

Zvinhu zvinotyisa

Zvikonzero zvekukonzera chirwere ichi hazvizivikanwi zvizere.


Zvimwe zvinokonzeresa pathologies zvinogona kuwedzera njodzi mukukura kwechirwere, senge; Down syndrome, cleidocranial dysplasia, nezvimwewo, izvi zvinongobata vashoma varwere.

Mukuwedzera, kufungirwa kwekutapurira kwechirwere kumwana kwakaiswa mberi nemasayendisiti. Mupfungwa iyi, kuvapo kwekuchinja kwemajini kune mamwe majini, muvabereki, kunogona kuvaita imwe njodzi yekuwedzera chirwere.

Kudzivirira uye kurapwa

Kuongororwa kwechirwere kunoitwa nenzira yakasiyana, maererano nemhando dzakasiyana-siyana dzakabatana.

The Beighton test inobva yaita kuti zvikwanise kuongorora kukanganisa kwechirwere pakufamba kwemamhasuru. Muedzo uyu une bvunzo dze5 dzakatevedzana. Izvi zvinosanganisira:

- nzvimbo yechanza cheruoko pasi apo uchichengeta makumbo akatwasuka;

- kotamisa gokora rimwe nerimwe kumashure;

- pfugama ibvi rimwe nerimwe kumashure;

– kotamisa chigunwe chakananga kuruoko;

– kotamisa kagunwe kumashure nekupfuura 90 °.

Muchirevo chechikamu cheBeighton chikuru kupfuura kana kuenzana ne4, nyaya yacho inogona kutambura ne hyperlaxity.

Kuongororwa ropa uye x-rays inogonawo kudiwa mukuongororwa kwechirwere. Idzi nzira dzinoita kuti zvikwanise kunyanya kuratidza kukura kwerheumatoid arthritis.

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