Mishonga yekurapa ye sickle cell anemia

Supplementation. Kuwedzerwa kwezuva nezuva nefolic acid (kana vhitamini B9) kwakakosha kusimudzira kugadzirwa kwemasero matsvuku eropa matsva.

Hydroxyurea. Pakutanga, waiva mushonga unorwisa leukemia, asi wakanga uriwo mushonga wokutanga wakawanikwa uchishanda mukurapa sickle cell anemia muvanhu vakuru. Kubva 1995, yave ichizivikanwa kuti inogona kuderedza kuwanda kwekurwiswa kunorwadza uye acute chest syndrome. Varwere vanoshandisa mushonga uyu havadiwo kuwedzerwa ropa.

Uyezve, kushandiswa kwakabatanidzwa kwehydroxyurea uye erythropoietin kuchawedzera kushanda kwehydroxyurea. Majekiseni esynthetic erythropoietin anoshandiswa kukurudzira kugadzirwa kwemasero matsvuku eropa uye kubvisa kuneta. Zvisinei, zvishoma zvinozivikanwa pamusoro pekuita kwayo kwenguva refu, kunyanya nekuda kwengozi yekudonha kune ngozi kwemazinga eropa. Kushandiswa kwaro kuvana vane sickle cell chirwere kuchiri kudzidzwa.

Kuisirwa ropa. Nokuwedzera nhamba yemasero matsvuku eropa anotenderera, kuisirwa ropa kunodzivirira kana kurapa zvimwe zvinetso zvechirwere chesickle cell. Muvana, vanobatsira kudzivirira sitiroko kudzokorora uye kuwedzera kwespleen.

Zvinokwanisika kudzokorora kuwedzerwa ropa, zvino zvakakosha kurapwa kuderedza ropa resimbi.

sejari

Kuvhiya kwakasiyana-siyana kunogona kuitwa kana matambudziko amuka. Somuenzaniso, tinogona:

-Bata mamwe marudzi emaronda e organic.

– Bvisa nduru.

- Isa prosthesis yehudyu mune chiitiko chehudyu necrosis.

- Dzivirira matambudziko emaziso.

-Ita maronda eganda kurapa maronda emakumbo kana akasapora, nezvimwe.

Kana iri pfupa rekuisa pfupa, dzimwe nguva rinoshandiswa mune vamwe vana kana paine zviratidzo zvakanyanya. Kupindira kwakadaro kunogona kurapa chirwere, asi kunopa njodzi dzakawanda pasina kufunga nezvekudiwa kwekuwana mupi akakodzera kubva kuvabereki vakafanana.

NB Mishonga mitsva yakawanda iri kuongororwa. Izvi ndizvo zvinonyanya kuitika nejene therapy, izvo zvinoita kuti zvikwanise kupa kusashanda kana kugadzirisa gene rakashata.

Mukudzivirira matambudziko

Incentive spirometer. Kuti vadzivise zvinetso zvemapapu, avo vane musana kana kuti chipfuva chakanyanya kurwadza vangada kushandisa inducing spirometer, mudziyo unovabatsira kufema zvakanyanya.

mishonga. Nemhaka yengozi dzakakomba dzine chokuita nezvirwere zvepneumococcal muvana vanobatwa, vanorayirwa penicillin kubva pakuberekwa kusvika pazera remakore matanhatu. Kuita uku kwakaderedza zvikuru kufa kwevanhu muzera iri. Mishonga inorwisa mabhakitiriya ichashandiswawo kudzivirira kutapukira muvakuru.

vaccination. Varwere vesickle cell - vana kana vakuru - vanofanirwa kuzvidzivirira zvakanyanya kubva kumabayo, furuwenza uye hepatitis. Kubayiwa kwejekiseni nguva dzose kunokurudzirwa kubva pakuzvarwa kusvika pazera remakore matanhatu.

Kana iri acute crisis

Marwadzo anoderedza. Izvo zvinoshandiswa kurwisa marwadzo muchiitiko chekurwisa kwakanyanya. Zvichienderana nenyaya yacho, murwere anogona kugutsikana ne-over-the-counter pain relievers kana kurongerwa mamwe ane simba.

Oxygen kurapa. Muchiitiko chekurwisa kwakanyanya kana matambudziko ekufema, kushandiswa kwemasikisi okisijeni kunoita kuti zvive nyore kufema.

Kudzorera mvura mumuviri. Muchiitiko chekurwisa kunorwadza, intravenous infusions inogonawo kushandiswa.

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