Omphalocele uye laparoschisis maitiro ekuzvarwa anooneka nekuremara pakuvhara madziro edumbu re "fetus", yakabatana nekunze (herniation) yechikamu chedumbu rayo. Uku kukanganiswa kunoda kutariswa kwakasarudzika pakuzvarwa uye kuvhiyiwa kubatanidza viscera mudumbu. The prognosis yakanaka muzviitiko zvakawanda.

tsananguro

Omphalocele uye laparoschisis icongenital anomalies inoonekwa nekutadza kuvhara mudhuri wedumbu re "fetus".

Iyo omphalocele inoratidzwa nekuvhura kwakawedzera kana kushoma mumadziro edumbu, pakati peguvhu, kuburikidza nechikamu cheura uye dzimwe nguva chiropa chinobuda kubva mudumbu remukati, kuumba inonzi hernia. Kana kukanganisa kwekuvhara madziro kwakakosha, hernia iyi inogona kunge iine inenge yese yemudumbu uye chiropa.

The exteriorized viscera inodzivirirwa ne "bhegi" rine danda reamniotic membrane uye jira re peritoneal membrane.

Kazhinji, omphalocele inosanganiswa nehumwe hurema hwekuzvarwa:

• kazhinji kukanganisa kwemoyo,
• genitourinary kana cerebral abnormalities,
• gastrointestinal atresia (kureva chidimbu kana kuvharika zvachose)…

Muvana vane laparoschisis, chirema chemudhuri chinowanikwa kurudyi rweguvhu. Iyo inoperekedzwa nehenia yemudumbu mudiki uye mune zvimwe zviitiko zveimwe viscera (colon, dumbu, kashoma dundira uye ovaries).

Ura, uhwo husina kuvharwa ne membrane inodzivirira, hunoyangarara zvakananga muamniotic fluid, zvikamu zveweti zvinowanikwa mumvura iyi zvinokonzeresa maronda ekuputika. Zvakasiyana-siyana zvemukati zvemukati zvinogona kuitika: kugadziridzwa uye kukora kwemadziro emukati, atresias, nezvimwe.

Kazhinji, hapana humwe hurema hunobatanidzwa.

Zvinokonzera

Hapana chikonzero chaicho chekuvharwa kwechikanganiso chemadziro emimba chinoratidzwa apo omphalocele kana laparoschisis inoratidzika iri yega.

Zvisinei, munenge chikamu chetatu kusvika hafu yezviitiko, omphalocele chikamu chepolymalformative syndrome, inowanzobatanidzwa ne trisomy 18 (imwe yekromosome 18), asiwo nemamwe maitiro echromosomal akadai se trisomy 13 kana 21, monosomy X (a. X chromosome imwe pane peya yemakromozomu ebonde) kana triploidy (kuvapo kweimwe batch yemakromozomu). Inenge kamwe chete mu10 chirwere chinobva kune imwe nzvimbo yegene defect (kunyanya omphalocele yakabatana neWiedemann-Beckwith syndrome). 

chirwere

Izvi zvisizvo zviviri zvinogona kuratidzwa pa ultrasound kubva pachikamu chekutanga chekuzvitakura, kazhinji zvichibvumira kuongororwa kwepamuviri.

Vanhu vane hanya

Epidemiological data inosiyana pakati pezvidzidzo.

Sekureva kwePublic Health France, mumabhuku matanhatu echiFrench ekuzvarwa anomalies, mukati menguva 2011 - 2015, omphalocele yakakanganisa pakati pe3,8 uye 6,1 kuberekwa kubva pagumi uye laparoschisis pakati pe10 uye 000 kuberekwa mu1,7.

Zvinhu zvinotyisa

Kunonoka kubata pamuviri (mushure memakore makumi matatu nemashanu) kana kuburikidza ne in vitro fertilization kunowedzera njodzi ye omphalocele.

Mungozi yezvakatipoteredza zvakadai sefodya yaamai kana kushandiswa kwecocaine inogona kubatanidzwa mu laparoschisis.

Antenatal therapeutic maitiro

Kuti udzivise maronda akawandisa emudumbu mumwana ane laparoschisis, zvinokwanisika kuita amnio-infusions (kutungamirirwa kweserum physiological mu amniotic cavity) panguva yechitatu trimester yekuzvitakura.

Pamamiriro maviri aya, kuchengetwa kwehunyanzvi nechikwata chemhando dzakasiyana-siyana chinosanganisira nyanzvi mukuvhiya kwevana uye kumutsiridza mwana mucheche kunofanirwa kurongeka kubva pakuzvarwa kuitira kudzivirira njodzi huru dzehutachiona uye kutambura kweura, kusanganisira mhedzisiro inouraya.

Kuendesa kwakakonzerwa kunowanzo kurongerwa kufambisa manejimendi. Kune omphalocele, kusununguka kwemukadzi kunowanzodiwa. Chikamu cheCesarean chinowanzosarudzwa kune laparoschisis. 

sejari

Kuvhiya manejimendi kwevacheche vane omphalocele kana laparoschisis ine chinangwa chekubatanidza nhengo mugomba redumbu uye kuvhara kuvhura mumadziro. Inotanga achangozvarwa. Nzira dzakasiyana dzinoshandiswa kuderedza njodzi yehutachiona.

Dumbu redumbu rinoramba risina chinhu panguva yekuzvitakura harisi nguva dzose yakakura zvakakwana kuti igare nhengo dze herniated uye zvinogona kuva zvakaoma kuivhara, kunyanya kana mwana muduku ane omphalocele yakakura. Izvo zvino zvakakosha kuenderera mberi nekubatanidzwazve zvishoma nezvishoma kwakapararira kwemazuva akati wandei, kana kunyange mavhiki akati wandei. Mhinduro dzenguva pfupi dzinogamuchirwa kuchengetedza viscera.

Evolution uye prognosis

Zvinetso zvinotapukira uye zvekuvhiya hazvigone kudziviswa nguva dzose uye kuramba uchinetseka, kunyanya kana chiitiko chekugara muchipatara kwenguva refu.

Omphalocèle

Kudzoreredzwa mugomba redumbu rakadzika reomphalocele hombe kunogona kukonzera kushushikana kwekufema mumwana. 

Kune vamwe vose, kufungidzira kweomphalocele yakaparadzaniswa kune imwe nzvimbo yakanaka, nekukurumidza kukurumidza kwekudya nemuromo uye kurarama kusvika kune rimwe gore rehuwandu hwakawanda hwevana, vanozokura zvakakwana. Muchiitiko chekukanganisa kwakabatana, chirevo chacho chakanyanya kuipa nehuwandu hwekufa, iyo inosvika 100% mune mamwe syndromes.

Laparochisis

Mukusavapo kwezvinetso, kufungidzira kwe laparoschisis kunonyanya kubatanidzwa nehutano hwehutano hwehuku. Zvinogona kutora mavhiki akati wandei kuti hunyanzvi hwemotokari uye kubatwa kwematumbo kupora. Kudya kwevabereki (nekupinza) kunofanirwa kuitwa. 

Vapfumbamwe kubva mugumi vacheche vari vapenyu mushure megore rimwe uye kune vakawanda, hapazovi nemigumisiro muupenyu hwezuva nezuva.